The Turkish Journal of Pediatrics 2010 , Vol 52 , Num 5
Pseudotumor Cerebri in a Child with Hyperimmunoglobulin E Syndrome
Departments of Pediatric Neurology, and Pediatric Immunology, Çukurova University Faculty of Medicine, Adana, Turkey İncecik F, Hergüner MÖ, Altunbaşak Ş, Yılmaz M. Pseudotumor cerebri in a child with hyperimmunoglobulin E syndrome. Turk J Pediatr 2010;52: 546-547.

Hyperimmunoglobulin E syndrome (HIES) is recognized as a multisystem disorder with various connective tissue, skeletal and immunologic abnormalities. Central nervous system abnormalities have been considered a feature of HIES. Pseudotumor cerebri (PTC) is a condition characterized by increased intracranial pressure in the absence of any intracranial mass lesion or ventricular dilatation, with normal neurology and cerebral spinal fluid composition. PTC without papilledema is rarely reported in children. We describe an atypical presentation of PTC in a child with HIES. Keywords : hyperimmunoglobulin E syndrome, pseudotumor cerebri, children

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