The Turkish Journal of Pediatrics 2020 , Vol 62 , Num 2
Persistence of right umbilical vein: a singular case
Giovanni Pinna 1 ,Maria Pia De Carolis 1 ,Antonio Lanzone 1 ,Gelsomina Del Sordo 1 ,Angela Botta 2 ,Sara De Carolis 2
1 Departments of Pediatrics, Fondazione Policlinico Gemelli IRCCS, Università Cattolica del Sacro Cuore Largo Francesco Vito 1, 00168 Rome, Italy
2 Departments of Obstetrics, Gynaecology, Fondazione Policlinico Gemelli IRCCS, Università Cattolica del Sacro Cuore, Largo Francesco Vito 1, 00168 Rome, Italy
DOI : 10.24953/turkjped.2020.02.024 Background. Persistent right umbilical vein (PRUV) is one of the most common prenatally detected venous anomaly. In the intrahepatic variant (I-PRUV) the right umbilical vein fuses with right portal vein and through the ductus venous drains into inferior vena cava, while in the uncommon extrahepatic variant (E-PRUV), the vein bypasses the liver completely. E-PRUV has a worse prognosis compared to I-PRUV, due either to severe hemodynamic effects or to the frequent association with other severe fetal malformations.

Case. Here we report a case of E-PRUV with good outcome. Prenatal fetal ultrasonography (US) performed at 33 weeks of gestation in 28-year old woman, highlights the presence of E-PRUV with right UV draining in inferior vena cava. In the male neonate born at 35 weeks of gestation by C-section, the Apgar Score was 95`- 1010 and no other associated malformations and hemodynamic decompensation were found. Postnatal abdominal US showed the presence of enlarged paraumbilical veins.

Conclusions. The association of E-PRUV draining into the inferior vena cava with shunt through paraumbilical veins, could have preserved offspring by severe cardiac overload, positively affecting prognosis. Keywords : persistent right umbilical vein, fetus, neonate

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