The Turkish Journal of Pediatrics 2018 , Vol 60 , Num 3
A case of steroid-resistance Hashimoto's encephalopathy presenting with sensorimotor polyneuropathy
Serhat Emeksiz 1 ,Nurettin Onur Kutlu 1 ,Nuri Alaçakır 1 ,Hüseyin Çaksen 2
1 Division of Pediatric Critical Care, Necmettin Erbakan University, Meram Faculty of Medicine, Konya, Turkey
2 Division of Pediatric Neurology, Department of Pediatrics, Necmettin Erbakan University, Meram Faculty of Medicine, Konya, Turkey
DOI : 10.24953/turkjped.2018.03.012 Emeksiz S, Kutlu NO, Alaçakır N, Çaksen H. A case of steroid-resistance Hashimoto's encephalopathy presenting with sensorimotor polyneuropathy. Turk J Pediatr 2018; 60: 310-314.

Hashimoto`s encephalopathy (HE) is a rare, auto-immune disease characterized by symptoms of acute or subacute encephalopathy associated with increased anti-thyroid antibody levels. The course of most HE cases is relapsing and remitting, which is similar to that of vasculitis and stroke. Steroids are the first line treatment in HE. In steroid non-responders other immunomodulatory therapies or plasmapheresis could be applied. We report a case of steroid-resistance HE with sensorimotor polyneuropathy, as a rare presentation of this disorder. Our case showed that HE may present with sensorimotor polyneuropathy; therefore HE should be considered in the differential diagnoses of polyneuropathy. Keywords : steroid-resistance Hashimoto`s encephalopathy,sensorimotor polyneuropathy, plasmapheresis, cyclophosphamide, auto-immune disease

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