The Turkish Journal of Pediatrics 2014 , Vol 56 , Num 6
Camptodactyly-Arthropathy-Coxa Vara-Pericarditis (CACP) Syndrome
1Department of Cardiovascular Surgery, Divisions of 2Pediatric Cardiology, and 3Pediatric Intensive Care, Department of Pediatrics, Ankara University Faculty of Medicine, Ankara, Turkey. E-mail: Camptodactyly-arthropathy-coxa vara-pericarditis (CACP) syndrome is a rare autosomal recessive congenital disorder that includes childhood-onset camptodactyly, synovial hyperplasia-related arthropathy, progressive coxa vara deformity and noninflammatory pericarditis. A seven-year-old male patient had a diagnosis of CACP. He had pericardial effusion and underwent surgical tube drainage. CACP syndrome is seen very rarely, and differential diagnosis is very important. CACP is usually treated medically, but surgery may sometimes be preferred, as in our patient. Keywords : pericarditis, familial arthropathy, camptodactyly
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