The Turkish Journal of Pediatrics
2013 , Vol 55 , Num 4
Late Neonatal Hypocalcemic Tetany as a Manifestation of Unrecognized Maternal Primary Hyperparathyroidism
Divisions of 1Neonatology and 2Pediatric Endocrinology, Department of Pediatrics, Ankara University Faculty of Medicine,
Ankara, Turkey. E-mail: drufukcakir@hotmail.com
Maternal primary hyperparathyroidism causing hypercalcemia during pregnancy
can suppress fetal and neonatal parathyroid hormone secretion. We report
a newborn with transient hypoparathyroidism presented by hypocalcemic
seizure and tetany on the 21st postnatal day in whom the final diagnosis was
asymptomatic maternal primary hyperparathyroidism. Neonatal hypocalcemia
usually occurs early in life in infants of maternal primary hyperparathyroidism,
and although it is very rare, further investigation for unexplained late-onset
hypocalcemia may reveal this diagnosis.
Keywords :
neonatal hypocalcemia, neonatal seizure, hypocalcemic tetany, primary
hyperparathyroidism, pregnancy, transient hypoparathyroidism.