The Turkish Journal of Pediatrics
2012 , Vol 54 , Num 4
Coexistence of left ventricular noncompaction and doubleorifice mitral valve in a patient with congestive heart failure
Division of Pediatric Cardiology, Department of Pediatrics, Ankara University Faculty of Medicine, Ankara, Turkey.
E-mail: fikridemir@yahoo.com
Left ventricular noncompaction (LVNC) is a rare cardiomyopathy. It usually
presents with ventricular dysfunction, thromboembolic events and arrhythmias.
An asymptomatic clinical course is also possible. LVNC is frequently associated
with other congenital heart diseases including heart valve abnormalities. The
coexistence of LVNC with double-orifice mitral valve was observed rarely.
The presence of such coexistence in a patient presented with heart failure
in the newborn period is reported herein because of its rarity.
Keywords :
noncompaction cardiomyopathy, double-orifice mitral valve, heart failure.