The Turkish Journal of Pediatrics 2020 , Vol 62 , Num 1
A rare presentation of adrenal adenoma in infancy: isolated Cushing`s syndrome
Oğuzhan Şal 1 ,Gülçin Yeğen 2 ,Pelin Oğuzkurt 3
1 Koç University School of Medicine, İstanbul, Turkey
2 Department of Pathology, İstanbul University İstanbul Faculty of Medicine, İstanbul, Turkey
3 Department of Pediatric Surgery, Koç University School of Medicine, İstanbul, Turkey
DOI : 10.24953/turkjped.2020.01.022 Adrenocortical tumors are rare in children. Most of these tumors present with endocrinological manifestations, majority of which with virilizing features alone or in combination with over production of other adrenal hormones. However, it is uncommon of an adrenocortical tumor to present solely with Cushing`s syndrome. In this paper we discuss the clinical presentation and management of a 5-month-old infant who had presented with Cushing`s syndrome due to a functioning adrenocortical adenoma without androgen and mineralocorticoid excess, and made a brief review on the clinical and histopathological characteristics of adrenocortical tumors. Keywords : adrenocortical, adenoma, Cushing's syndrome, non-virilizing, wieneke
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