The Turkish Journal of Pediatrics 2018 , Vol 60 , Num 4
Percutaneous embolization of congenital portosystemic venous shunt in an infant with respiratory distress
Fatoş Alkan 1 ,Fatih Düzgün 2 ,Hasan Yüksel 3 ,Serdar Tarhan 2 ,Şenol Coşkun 1
1 Division of Pediatric Cardiology, Celal Bayar University, School of Medicine, Manisa, Turkey
2 Department of Radiology, Celal Bayar University, School of Medicine, Manisa, Turkey
3 Division of Pediatric Allergy and Pulmonology Department of Pediatrics, Celal Bayar University, School of Medicine, Manisa, Turkey
DOI : 10.24953/turkjped.2018.04.019 Alkan F, Düzgün F, Yüksel H, Tarhan S, Coşkun Ş. Percutaneous embolization of congenital portosystemic venous shunt in an infant with respiratory distress. Turk J Pediatr 2018; 60: 456-459.

A 5-month-old boy with progressive respiratory distress was admitted to our hospital. Physical examination revealed mild tachypnea and retraction. The left main bronchus was found as severely collapsed between the right pulmonary artery and the descending aorta, on the bronchoscopic evaluation. Further evaluation revealed persistent ductus venosus (PDV). As in the fetal period the ductus venosus arises from the posterior aspect of the left portal vein, a PDV is considered another type of intrahepatic portosystemic shunt. Therefore, he was diagnosed with congenital portosystemic venous shunt, leading to persistent respiratory distress. The PDV was closed with Amplatzer vascular plug II, and then he had immediate clinical improvement. Congenital portosystemic venous shunts (CPSS) are rare vascular malformations associated with severe complications. Here we presented a case with progressive respiratory distress as a result of CPSS and rapid improvement after embolization. Keywords : portosystemic venous shunt, persistent ductus venosus, amplatzer vascular plug II.

Copyright © 2016 turkishjournalpediatrics.org