The Turkish Journal of Pediatrics
2012 , Vol 54 , Num 5
Nasal Congenital Fibrolipomatous Hamartoma in a Premature Infant
Division of 1Neonatology, Zekai Tahir Burak Maternity Training Hospital and Departments of 2Otorhinolaryngology-Head
and Neck Surgery, and 3Pathology, Hacettepe University Faculty of Medicine, Ankara, Turkey. E-mail: dryekta@gmail.com
Hamartomas are tumor-like lesions composed of tissue elements normally
found at the site where they are located, but which grow in a disorganized
manner. They generally occur at birth or soon after, although presentations
during adult life have been reported. Hamartomas of the head and neck are
very rare. The exact mechanisms behind the development of hamartomas
remain unknown; however, their benign nature renders complete surgical
excision sufficient for their management. Here, we describe a case of a
premature infant with a hamartomatous polypoid lesion containing both
fibrous and adipose components, originating from the dorsum of the nose.
The differential diagnosis and management of hamartomas of the head
and neck are also discussed. Although several cases series on precalcaneal
fibrolipomatous hamartomas have been encountered in the literature, to the
best of our knowledge, this is the first report of a nasally located congenital
fibrolipomatous hamartoma.
Keywords :
fibrolipomatous hamartoma, nose, premature infant.