A rare form of Guillain-Barré syndrome: pharyngeal-cervical-brachial variant
M. Özlem Hergüner, Tugay Tepe, Şakir Altunbaşak, Vildan Baytok
Department of Pediatric Neurology, Çukurova University Faculty of Medicine, Adana, Turkey
Hergüner MÖ, Tepe T, Altunbaşak Ş, Baytok V. A rare form of
Guillain-Barré syndrome: pharyngeal-cervical-brachial variant. Turk J Pediatr
2008; 50: 91-93.
Guillain-Barré syndrome is clinically characterized by acute onset of generalized,
symmetrical, and ascending muscle weakness and areflexia from peripheral
nerve involvement. In Guillain-Barré syndrome variants, however, some patients
have unusual distribution of muscle involvement. Pharyngeal-cervical-brachial
variant of Guillain-Barré syndrome is characterized by oropharyngeal, neck,
and upper limb muscle involvement. Although Guillain-Barré syndrome is
one of several post-infectious diseases that cause limb muscle weakness,
the incidence of pharyngeal-cervical-brachial variant is relatively low. Here
we report the case of a 16-month-old boy who developed a rare form of
Guillain-Barré syndrome, the pharyngeal-cervical-brachial variant of the disease.
We concluded that taking all the other etiologic reasons into consideration,
pharyngeal-cervical-brachial variant of Guillain-Barré syndrome should be
remembered in patients with symptoms of bulbar and upper extremity
weakness not only for early diagnosis but also to plan the treatment early
and follow up the potential complications.